DBS for Dystonia
Dystonia is a movement disorder that affects about 300,000 Americans. Simple activities like walking, balancing, or even talking are hard for these patients. Now – a surgery that’s known for helping people with Parkinson’s is also helping those with dystonia.
Emma Horton is a little girl with a big personality.
“She lights up a room when she goes into it,” Cheryl Horton, Emma’s mom, told Ivanhoe.
Even though the seven-year-old can’t talk –she can communicate with her iPad.
“My favorite movie is ‘Frozen,’” Emma told Ivanhoe.
Emma has dystonia, a condition that causes her muscles to contract and spasm. Even the simplest tasks are a challenge.
“Just little things that you take for granted that a 7-year-old should be able to do, Emma was never able to do it,” Colby Horton, Emma’s dad, told Ivanhoe.
But today Emma is doing better than ever – thanks to deep brain stimulation, DBS for short.
“We’ve been very pleasantly surprised by her,” John Honeycutt, MD, Neurosurgeon, Cook Children’s Medical Center, told Ivanhoe.
Here’s how it works: electrodes are placed in the brain and wires connect them to batteries implanted in the chest. The device sends electrical pulses to affected parts of the brain – and “resets” them. The best part is Emma was able to have anesthesia and be asleep during the surgery.
“We used to keep the kids awake. They don’t have to be awake anymore,” Dr. Honeycutt said. “We saw immediately some of that undesired movement stop.”
Also, three months after DBS, Emma rode her bike for the first time.
Dr. Honeycutt says it typically takes six months or longer for patients with dystonia to see very good results after DBS. Emma is expected to improve even more. Although DBS is a promising treatment, it isn’t a cure. If patients have their device removed – their symptoms will likely return.